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Search Results to Ronald J Sokol

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Sokol, Ronald

One or more keywords matched the following properties of Sokol, Ronald

Property	Value
full name	Ronald J Sokol
keywords	Childhood Liver Disease
keywords	Metabolic Liver Disease
keywords	Wilson Disease
keywords	Parenteral Nutrition Associated Liver Disease
label	Sokol, Ronald
last name	Sokol

One or more keywords matched the following items that are connected to Sokol, Ronald

Item Type	Name
Award or Honor Receipt	James E. Strain M.D. Award in Pediatrics
Award or Honor Receipt	Harry Shwachman Award
Award or Honor Receipt	Arnold Silverman, MD Endowed Chair in Digestive Health
Award or Honor Receipt	Alpha Omega Alpha
Award or Honor Receipt	Mead Johnson Award for Nutritional Research
Award or Honor Receipt	2003 Nutrition Award
Award or Honor Receipt	Hall of Honor
Academic Article	Vitamin E deficiency in adults with chronic liver disease.
Academic Article	Frequency and clinical progression of the vitamin E deficiency neurologic disorder in children with prolonged neonatal cholestasis.
Academic Article	Improved neurologic function after long-term correction of vitamin E deficiency in children with chronic cholestasis.
Academic Article	Orthotopic liver transplantation for acute fulminant Wilson disease.
Academic Article	Vitamin E deficiency during chronic childhood cholestasis: presence of sural nerve lesion prior to 2 1/2 years of age.
Academic Article	Vitamin E toxicity.
Academic Article	Mechanism causing vitamin E deficiency during chronic childhood cholestasis.
Academic Article	Comparison of vitamin E and 25-hydroxyvitamin D absorption during childhood cholestasis.
Academic Article	Vitamin E deficiency with normal serum vitamin E concentrations in children with chronic cholestasis.
Academic Article	An unusual presentation of Wegener's granulomatosis mimicking inflammatory bowel disease.
Academic Article	Normal vitamin E status in spinal muscular atrophy.
Academic Article	Grade I Reye's syndrome. A frequent cause of vomiting and liver dysfunction after varicella and upper-respiratory-tract infection.
Academic Article	Renal abnormalities in arteriohepatic dysplasia and nonsyndromic intrahepatic biliary hypoplasia.
Academic Article	An erysipelas-like scalp cellulitis due to haemophilus influenzae type b.
Academic Article	Anastomotic ulceration: a late complication of ileocolonic anastomosis.
Academic Article	Outcome of syndromic paucity of interlobular bile ducts (Alagille syndrome) with onset of cholestasis in infancy.
Academic Article	Altered coding for a strictly conserved di-glycine in the major bilirubin UDP-glucuronosyltransferase of a Crigler-Najjar type I patient.
Academic Article	Oxidant injury to hepatic mitochondria in patients with Wilson's disease and Bedlington terriers with copper toxicosis.
Academic Article	Association of paucity of interlobular bile ducts with prune belly syndrome.
Academic Article	Association of cytomegalovirus with Ménétrier's disease in childhood: report of two new cases with a review of literature.
Academic Article	Abnormal hepatic mitochondrial respiration and cytochrome C oxidase activity in rats with long-term copper overload.
Academic Article	Antioxidants in pediatric gastrointestinal disease.
Academic Article	Familial occurrence of cavernous transformation of the portal vein.
Academic Article	Hepatic concentrations of zinc, copper and manganese in infants with extrahepatic biliary atresia.
Academic Article	An international symposium on Wilson's and Menkes' diseases.
Academic Article	Antioxidant defenses in metal-induced liver damage.
Academic Article	Translocation of apolipoprotein B across the endoplasmic reticulum is blocked in abetalipoproteinemia.
Academic Article	Congenital nonchylous ascites due to intestinal malrotation.
Academic Article	Management of esophageal varices in children by endoscopic variceal ligation.
Academic Article	When is an amniocentesis for fetal maturity unnecessary in nondiabetic pregnancies at risk?
Academic Article	Intrahepatic "cholestasis facies": is it specific for Alagille syndrome?
Academic Article	Quinacrine hydrochloride-induced yellow discoloration of the skin in children.
Academic Article	Vitamin E reduces oxidant injury to mitochondria and the hepatotoxicity of taurochenodeoxycholic acid in the rat.
Academic Article	A position paper of the North American Society for Pediatric Gastroenterology and Nutrition. Pediatric gastroenterology Workforce Survey and future supply and demand.
Academic Article	Total parenteral nutrition-related liver disease.
Academic Article	Effect of oxypurinol, a xanthine oxidase inhibitor, on hepatic injury in the bile duct-ligated rat.
Academic Article	Effect of ursodeoxycholic acid therapy on hepatic function in children with intrahepatic cholestatic liver disease.
Academic Article	Fat-soluble vitamins and their importance in patients with cholestatic liver diseases.
Academic Article	Detection of reovirus RNA in hepatobiliary tissues from patients with extrahepatic biliary atresia and choledochal cysts.
Academic Article	Mitochondria and childhood liver diseases.
Academic Article	Alagille syndrome: A nutritional niche for Notch.
Academic Article	Recommendations for management of liver and biliary tract disease in cystic fibrosis. Cystic Fibrosis Foundation Hepatobiliary Disease Consensus Group.
Academic Article	Correction of hypozincemia following liver transplantation in children is associated with reduced urinary zinc loss.
Academic Article	How many wrongs make a right (or a left)? Vertebrate asymmetry unraveled.
Academic Article	The effect of idebenone, a coenzyme Q analogue, on hydrophobic bile acid toxicity to isolated rat hepatocytes and hepatic mitochondria.
Academic Article	Disorders of the mitochondria.
Academic Article	Identification of a new inborn error in bile acid synthesis: mutation of the oxysterol 7alpha-hydroxylase gene causes severe neonatal liver disease.
Academic Article	At long last: an animal model of Wilson's disease.
Academic Article	Pancreatic insufficiency, growth, and nutrition in infants identified by newborn screening as having cystic fibrosis.
Academic Article	Evidence for involvement of oxygen free radicals in bile acid toxicity to isolated rat hepatocytes.
Academic Article	Liver disease in Navajo neuropathy.
Academic Article	Impaired discrimination between stereoisomers of alpha-tocopherol in patients with familial isolated vitamin E deficiency.
Academic Article	Liver transplantation in mitochondrial respiratory chain disorders.
Academic Article	Multicenter trial of d-alpha-tocopheryl polyethylene glycol 1000 succinate for treatment of vitamin E deficiency in children with chronic cholestasis.
Academic Article	Fulminant hepatitis associated with centrilobular hepatic necrosis in young children.
Academic Article	Long-term results with the Kasai operation for biliary atresia.
Academic Article	Supplementation with carotenoids corrects increased lipid peroxidation in children with cystic fibrosis.
Academic Article	Hepatoblastoma in a neonate: a hypervascular presentation mimicking hemangioendothelioma.
Academic Article	Biliary atresia: current concepts and research directions. Summary of a symposium.
Academic Article	alpha-tocopherol ameliorates oxidant injury in isolated copper-overloaded rat hepatocytes.
Academic Article	Survival after first esophageal variceal hemorrhage in patients with biliary atresia.
Academic Article	Navajo neurohepatopathy: a mitochondrial DNA depletion syndrome?
Academic Article	Cholangiocyte biology and cystic fibrosis liver disease.
Academic Article	Circulating antioxidant concentrations in children with inflammatory bowel disease.
Academic Article	Congenital bilary atresia: report of three cases, two occurring in one family. Whitten WW, Adie GC. J Pediatr 1952;40:539-48.
Academic Article	Response of elevated Epstein-Barr virus DNA levels to therapeutic changes in pediatric liver transplant patients: 56-month follow up and outcome.
Academic Article	Nitric oxide ameliorates hydrophobic bile acid-induced apoptosis in isolated rat hepatocytes by non-mitochondrial pathways.
Academic Article	Epstein-Barr virus and post-transplant lymphoproliferative disease.
Academic Article	Introduction to the pediatric liver research agenda: a blueprint for the future.
Academic Article	Cholestatic liver disease: Working Group Report of the First World Congress of Pediatric Gastroenterology, Hepatology, and Nutrition.
Academic Article	On the bile sludge syndrome or is total parenteral nutrition cholestasis a surgical disease?
Academic Article	ApoB gene nonsense and splicing mutations in a compound heterozygote for familial hypobetalipoproteinemia.
Academic Article	Early respiratory course in infants with cystic fibrosis: relevance to newborn screening.
Academic Article	Variability of biochemical and clinical phenotype in X-linked liver glycogenosis with mutations in the phosphorylase kinase PHKA2 gene.
Academic Article	Genetic induction of proinflammatory immunity in children with biliary atresia.
Academic Article	Urinary F2-isoprostanes in young healthy children at risk for type 1 diabetes mellitus.
Academic Article	Case report: nonalcoholic steatohepatitis in a teenage girl with type 2 diabetes.
Academic Article	Partial splenic embolization in five children with hypersplenism: effects of reduced-volume embolization on efficacy and morbidity.
Academic Article	Coordinate expression of regulatory genes differentiates embryonic and perinatal forms of biliary atresia.
Academic Article	Gastrointestinal manifestations of mitochondrial disease.
Academic Article	Biliary atresia is associated with CD4+ Th1 cell-mediated portal tract inflammation.
Academic Article	Liver involvement in Alpers disease.
Academic Article	Efficacy of statewide neonatal screening for cystic fibrosis by assay of trypsinogen concentrations.
Academic Article	Beta-carotene prevents bile acid-induced cytotoxicity in the rat hepatocyte: Evidence for an antioxidant and anti-apoptotic role of beta-carotene in vitro.
Academic Article	Amylopectinosis disease isolated to the heart with normal glycogen branching enzyme activity and gene sequence.
Academic Article	Portopulmonary hypertension in pediatric patients.
Academic Article	Human hepatic mitochondria generate reactive oxygen species and undergo the permeability transition in response to hydrophobic bile acids.
Academic Article	Characterization of acute liver failure and development of a continuous risk of death staging system in children.
Academic Article	Armed CD4+ Th1 effector cells and activated macrophages participate in bile duct injury in murine biliary atresia.
Academic Article	Biliary atresia: clinical profiles, risk factors, and outcomes of 755 patients listed for liver transplantation.
Academic Article	Comparison of indices of vitamin A status in children with chronic liver disease.
Academic Article	Connective tissue growth factor expression is increased in biliary epithelial cells in biliary atresia.
Academic Article	A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000.
Academic Article	Neonatal screening for biliary atresia.
Academic Article	Rotavirus infection frequency and risk of celiac disease autoimmunity in early childhood: a longitudinal study.
Academic Article	Cellular and humoral autoimmunity directed at bile duct epithelia in murine biliary atresia.
Academic Article	Acute hepatitis and liver failure associated with influenza A infection in children.
Academic Article	Antioxidants in cystic fibrosis. Conclusions from the CF antioxidant workshop, Bethesda, Maryland, November 11-12, 2003.
Academic Article	A pilot study on the safety and efficacy of a novel antioxidant rich formulation in patients with cystic fibrosis.
Academic Article	Subcutaneous vitamin E ameliorates liver injury in an in vivo model of steatocholestasis.
Academic Article	Screening and outcomes in biliary atresia: summary of a National Institutes of Health workshop.
Academic Article	Liver disease in mitochondrial disorders.
Academic Article	Colonic polyp as lead point for intussusception.
Academic Article	Oligoclonal expansions of CD4+ and CD8+ T-cells in the target organ of patients with biliary atresia.
Academic Article	Corticosteroid treatment in biliary atresia: Tonic or toast?
Academic Article	European biliary atresia registries: summary of a symposium.
Academic Article	The Multiple Facets of ABCB4 (MDR3) Deficiency.
Academic Article	Decreased total serum coenzyme-Q10 concentrations: a longitudinal study in children with cystic fibrosis.
Academic Article	Impaired ability of patients with familial isolated vitamin E deficiency to incorporate alpha-tocopherol into lipoproteins secreted by the liver.
Academic Article	Anthropometric evaluation of children with chronic liver disease.
Academic Article	Cutaneous photosensitivity and coproporphyrin abnormalities in the Alagille syndrome.
Academic Article	Comparison of total serum lipids measured by two methods.
Academic Article	Hepatic veno-occlusive disease and human herpes virus 7 infection in primary agammaglobulinemia.
Academic Article	Biliary atresia screening: why, when, and how?
Academic Article	Treatment of neonatal hemochromatosis with exchange transfusion and intravenous immunoglobulin.
Academic Article	Reloading against rare liver diseases.
Academic Article	Pulmonary vascular complications in asymptomatic children with portal hypertension.
Academic Article	Long term G-CSF-induced remission of ulcerative colitis-like inflammatory bowel disease in a patient with glycogen storage disease Ib and evaluation of associated neutrophil function.
Academic Article	Pitfalls in diagnosing galactosemia: false negative newborn screening following red blood cell transfusion.
Academic Article	Glutathione status of isolated rat hepatocytes affects bile acid-induced cellular necrosis but not apoptosis.
Academic Article	Vitamin E supplementation reduces the incidence of diabetes but not insulitis in NOD mice.
Academic Article	Design and validation of the biliary atresia research consortium histologic assessment system for cholestasis in infancy.
Academic Article	The chronic disease of childhood obesity: the sleeping giant has awakened.
Academic Article	The anatomic pattern of biliary atresia identified at time of Kasai hepatoportoenterostomy and early postoperative clearance of jaundice are significant predictors of transplant-free survival
Academic Article	Vitamin E deficiency neuropathy in children with fat malabsorption. Studies in cystic fibrosis and chronic cholestasis.
Academic Article	Bile acid-induced rat hepatocyte apoptosis is inhibited by antioxidants and blockers of the mitochondrial permeability transition.
Academic Article	American Liver Foundation releases Pediatric Liver Research Agenda-2000.
Academic Article	Emergence of fibroblasts with a proinflammatory epigenetically altered phenotype in severe hypoxic pulmonary hypertension.
Academic Article	Endoscopic dilation of an ileocolonic stricture in an infant with short gut syndrome.
Academic Article	Blastocystis hominis gastroenteritis in a hemophiliac with acquired immune deficiency syndrome.
Academic Article	Normal vitamin E status in sickle hemoglobinopathies in Colorado.
Academic Article	Liver cell injury and fibrosis.
Academic Article	Portal hypertension in children and young adults with biliary atresia.
Academic Article	Lack of correlation between infection with reovirus 3 and extrahepatic biliary atresia or neonatal hepatitis.
Academic Article	Inflammatory bowel disease in pediatric patients with cerebral palsy.
Academic Article	Clues to the etiology of bile duct injury in biliary atresia.
Academic Article	Copper toxicity and lipid peroxidation in isolated rat hepatocytes: effect of vitamin E.
Academic Article	Vitamin E deficiency and neurologic disease.
Academic Article	Medical management of the infant or child with chronic liver disease.
Academic Article	Vitamin E status in cholestasis.
Academic Article	Friedreich's disease: V. Variant form with vitamin E deficiency and normal fat absorption.
Academic Article	Hypoalbuminemia at diagnosis as a marker for severe respiratory course in infants with cystic fibrosis identified by newborn screening.
Academic Article	Treatment of vitamin E deficiency during chronic childhood cholestasis with oral d-alpha-tocopheryl polyethylene glycol-1000 succinate.
Academic Article	Tocopheryl polyethylene glycol 1000 succinate therapy for vitamin E deficiency during chronic childhood cholestasis: neurologic outcome.
Academic Article	Correction of vitamin E deficiency in children with chronic cholestasis. II. Effect on gastrointestinal and hepatic function.
Academic Article	New North American research network focuses on biliary atresia and neonatal liver disease.
Academic Article	Hepatic dysfunction following the Fontan procedure.
Academic Article	Effect of dietary lipid and vitamin E on mitochondrial lipid peroxidation and hepatic injury in the bile duct-ligated rat.
Academic Article	Vitamin E deficiency in cholestatic liver disease.
Academic Article	Vitamin E deficiency in adults.
Academic Article	Kasai procedure and vitamin E.
Academic Article	Clearance of chronic hepatitis B virus infection in young children after alpha interferon treatment.
Academic Article	Generation of hydroperoxides in isolated rat hepatocytes and hepatic mitochondria exposed to hydrophobic bile acids.
Academic Article	Ataxia with isolated vitamin E deficiency is caused by mutations in the alpha-tocopherol transfer protein.
Academic Article	A prospective study of the incidence of childhood celiac disease.
Academic Article	Biliary diversion for progressive familial intrahepatic cholestasis: improved liver morphology and bile acid profile.
Academic Article	Developmental changes in newborn lamb brain mitochondrial activity and postasphyxial lipid peroxidation.
Academic Article	Clinical features of children with screening-identified evidence of celiac disease.
Academic Article	Expanding spectrum of mitochondrial disorders.
Academic Article	Detection of group C rotavirus in infants with extrahepatic biliary atresia.
Academic Article	Interferon treatment for chronic hepatitis B: enhanced response in children 5 years old or younger.
Academic Article	Hepatic oxidant injury and glutathione depletion during total parenteral nutrition in weanling rats.
Academic Article	Enrichment of rat hepatic organelles by vitamin E administered subcutaneously.
Academic Article	Licorice compounds glycyrrhizin and 18beta-glycyrrhetinic acid are potent modulators of bile acid-induced cytotoxicity in rat hepatocytes.
Academic Article	Optimizing outcomes and bridging biliary atresia into adulthood.
Academic Article	Outcome after exploratory laparoscopy for unexplained abdominal pain in childhood.
Academic Article	Unraveling the pathogenesis and etiology of biliary atresia.
Academic Article	Increased susceptibility of fat-laden Zucker-rat hepatocytes to bile acid-induced oncotic necrosis: an in vitro model of steatocholestasis.
Academic Article	Fulminant Epstein-Barr viral hepatitis: orthotopic liver transplantation and review of the literature.
Academic Article	Hepato-portopulmonary disorders--not just in adults!
Academic Article	Safety, efficacy, and tolerance of intestinal lavage in pediatric patients undergoing diagnostic colonoscopy.
Academic Article	Use of rifampin for severe pruritus in children with chronic cholestasis.
Academic Article	Prospective, long-term study of fat-soluble vitamin status in children with cystic fibrosis identified by newborn screen.
Academic Article	Acute liver failure in children: the first 348 patients in the pediatric acute liver failure study group.
Academic Article	Transglutaminase antibodies in children with a genetic risk for celiac disease.
Academic Article	Health-related quality of life in pediatric liver transpant recipients compared to other chronic disease groups
Academic Article	Outcomes in children who underwent transplantation for autoimmune hepatitis
Academic Article	"Let there be bile"--understanding hepatic injury in cholestasis.
Academic Article	Role of oxidant stress in the permeability transition induced in rat hepatic mitochondria by hydrophobic bile acids.
Academic Article	Presentation of the 2006 Shwachman Award to Judith M. Sondheimer, MD.
Academic Article	Large-volume paracentesis in the management of ascites in children.
Academic Article	Noninfectious colitis associated with short gut syndrome in infants.
Academic Article	Improvement of cyclosporin absorption in children after liver transplantation by means of water-soluble vitamin E.
Academic Article	Etiopathogenesis of biliary atresia.
Academic Article	Hepatobiliary disease in neonatal lupus: prevalence and clinical characteristics in cases enrolled in a national registry.
Academic Article	Proliferation to paucity: evolution of bile duct abnormalities in a case of Alagille syndrome.
Academic Article	Niemann-pick disease type C in neonatal cholestasis at a North American Center.
Academic Article	Fat-soluble vitamins in infants identified by cystic fibrosis newborn screening.
Academic Article	Pathogenesis and outcome of biliary atresia: current concepts.
Academic Article	Autoantibodies in mothers of children with neonatal liver disease.
Academic Article	Re: Article by Kamath et al.-"Facial features in Alagille Syndrome".
Academic Article	Quantitation of rat liver vitamin E metabolites by LC-MS during high-dose vitamin E administration.
Academic Article	Selection bias and vitamin E status in cystic fibrosis.
Academic Article	Vitamin E and neurologic deficits.
Academic Article	Risk of celiac disease autoimmunity and timing of gluten introduction in the diet of infants at increased risk of disease.
Academic Article	Mitochondrial hepatopathies: advances in genetics and pathogenesis.
Academic Article	Configuration challenges: implementing translational research policies in electronic medical records.
Academic Article	The 2008 World Congress Working Group Reports: an opportunity for a worldwide consensus to affect children's digestive health.
Academic Article	Growth failure and outcomes in infants with biliary atresia: a report from the Biliary Atresia Research Consortium.
Academic Article	The future of pediatrics: a festschrift for M. Douglas Jones, Jr, MD.
Academic Article	Alpha-tocopherol regulation of hepatic cytochrome P450s and ABC transporters in rats.
Academic Article	Swiss outcomes in biliary atresia: are there lessons to be learned?
Academic Article	Hypoalbuminemia in young infants with cystic fibrosis.
Academic Article	Adoption of hepatitis B virus-infected foreign-born children.
Academic Article	Evaluation of a scoring system for assessing prognosis in pediatric acute liver failure.
Academic Article	Spontaneous perforation of the bile duct in a toddler: the role of endoscopic retrograde cholangiopancreatography in diagnosis and therapy.
Academic Article	Hepatitis B therapy in children.
Academic Article	Effect of vitamin E on transport processes in isolated rat hepatocytes.
Academic Article	Plasma micronutrients are associated with dietary intake and environmental tobacco smoke exposure in a paediatric population.
Academic Article	Failure of resolution of portal fibrosis during omega-3 fatty acid lipid emulsion therapy in two patients with irreversible intestinal failure.
Academic Article	Plasma manganese concentrations in infants and children receiving parenteral nutrition.
Academic Article	Mechanisms of disease: Inborn errors of bile acid synthesis.
Academic Article	Resistance of young rat hepatic mitochondria to bile acid-induced permeability transition: potential role of alpha-tocopherol.
Academic Article	Cardiopulmonary manifestations of portovenous shunts from congenital absence of the portal vein: pulmonary hypertension and pulmonary vascular dilatation.
Academic Article	Oxidant injury to hepatic mitochondrial lipids in rats with dietary copper overload. Modification by vitamin E deficiency.
Academic Article	Choledochoduodenostomy in pediatric liver transplantation.
Academic Article	The coming of age of vitamin E.
Academic Article	Vitamin E and neurologic function in man.
Academic Article	Parenteral nutrition supplementation in biliary atresia patients listed for liver transplantation.
Academic Article	Fat-soluble-vitamin status during the first year of life in infants with cystic fibrosis identified by screening of newborns.
Academic Article	Efficacy of fat-soluble vitamin supplementation in infants with biliary atresia.
Academic Article	Viral hepatitis in children.
Academic Article	Intestinal malabsorption of vitamin E in primary biliary cirrhosis.
Academic Article	Lack of tocopherol in peripheral nerves of vitamin E-deficient patients with peripheral neuropathy.
Academic Article	Assessing vitamin E status in childhood cholestasis.
Academic Article	No association of vitamin D intake or 25-hydroxyvitamin D levels in childhood with risk of islet autoimmunity and type 1 diabetes: the Diabetes Autoimmunity Study in the Young (DAISY).
Academic Article	Toll-like receptor 4-dependent Kupffer cell activation and liver injury in a novel mouse model of parenteral nutrition and intestinal injury.
Academic Article	Pulmonary function in individuals who underwent liver transplantation: from the US cystic fibrosis foundation registry.
Academic Article	Preparedness of the CTSA's structural and scientific assets to support the mission of the National Center for Advancing Translational Sciences (NCATS).
Academic Article	Pancreatic insufficiency is not a prevalent problem in Alagille syndrome.
Academic Article	Evaluation of the liver injury unit scoring system to predict survival in a multinational study of pediatric acute liver failure.
Academic Article	Vitamin E deficiency in neuropathy of abetalipoproteinemia.
Academic Article	Isolated vitamin E deficiency in the absence of fat malabsorption--familial and sporadic cases: characterization and investigation of causes.
Concept	Soybean Oil
Concept	Survival Rate
Concept	Virus Diseases
Concept	Genomic Library
Concept	Autoimmune Diseases
Concept	Oxidative Stress
Concept	Liver Diseases
Concept	Stigmasterol
Concept	Short Bowel Syndrome
Concept	Reactive Oxygen Species
Concept	Smoking
Concept	Diffuse Cerebral Sclerosis of Schilder
Concept	Longitudinal Studies
Concept	Solubility
Concept	Synapses
Concept	Biliary Tract Diseases
Concept	Microscopy, Electron, Scanning
Concept	Blotting, Southern
Concept	Diet, Sodium-Restricted
Concept	Pancreatic Diseases
Concept	Glycogen Storage Disease Type I
Concept	Disease Models, Animal
Concept	Substance-Related Disorders
Concept	Sequence Analysis, DNA
Concept	Granulocyte Colony-Stimulating Factor
Concept	Sulfasalazine
Concept	Mitochondrial Diseases
Concept	Parenteral Nutrition, Total
Concept	Intestinal Diseases
Concept	Health Services Accessibility
Concept	Nutrition Assessment
Concept	Multigene Family
Concept	Prostaglandin-Endoperoxide Synthases
Concept	Rupture, Spontaneous
Concept	Qb-SNARE Proteins
Concept	Educational Status
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Concept	Cross-Over Studies
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Concept	Disease Progression
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Concept	Kidney Diseases
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Concept	Selection Bias
Concept	Citrate (si)-Synthase
Concept	Genes, T-Cell Receptor beta
Concept	Cell Survival
Concept	Sicily
Concept	Single-Blind Method
Concept	Validation Studies as Topic
Concept	National Institute of Diabetes and Digestive and Kidney Diseases (U.S.)
Concept	Portal System
Concept	Genes, Mitochondrial
Concept	Succinate Cytochrome c Oxidoreductase
Concept	Spinal Cord Diseases
Concept	Life Style
Concept	Hirschsprung Disease
Concept	Survival Analysis
Concept	Tobacco Smoke Pollution
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Concept	Scalp Dermatoses
Concept	Celiac Disease
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Concept	Sex Factors
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Concept	Sequence Alignment
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Concept	Salmonella Infections
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Concept	Infant Nutritional Physiological Phenomena
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Award or Honor Receipt	Governing Board
Academic Article	Phytosterols promote liver injury and Kupffer cell activation in parenteral nutrition-associated liver disease.
Academic Article	Remote source document verification in two national clinical trials networks: a pilot study.
Academic Article	Health related quality of life in patients with biliary atresia surviving with their native liver.
Academic Article	Evaluation of the child with suspected mitochondrial liver disease.
Academic Article	Mitochondrial hepatopathies: advances in genetics, therapeutic approaches, and outcomes.
Academic Article	Obstructive sleep apnea and hypoxemia are associated with advanced liver histology in pediatric nonalcoholic fatty liver disease.
Academic Article	Significant hepatic involvement in patients with ornithine transcarbamylase deficiency.
Academic Article	Liver transplantation for pediatric metabolic disease.
Academic Article	Mutations in TJP2 cause progressive cholestatic liver disease.
Academic Article	Extrahepatic anomalies in infants with biliary atresia: results of a large prospective North American multicenter study.
Academic Article	Use of corticosteroids after hepatoportoenterostomy for bile drainage in infants with biliary atresia: the START randomized clinical trial.
Academic Article	High-dose IgG therapy mitigates bile duct-targeted inflammation and obstruction in a mouse model of biliary atresia.
Academic Article	Adventitial fibroblasts induce a distinct proinflammatory/profibrotic macrophage phenotype in pulmonary hypertension.
Academic Article	Alcohol abuse during pregnancy: an epidemiologic study.
Academic Article	Medical status of 219 children with biliary atresia surviving long-term with their native livers: results from a North American multicenter consortium.
Academic Article	Specific microbiome changes in a mouse model of parenteral nutrition associated liver injury and intestinal inflammation.
Academic Article	Lack of HLA predominance and HLA shared epitopes in biliary Atresia.
Academic Article	The effects of methadone treatment on the reactivity of the nonstress test.
Academic Article	Total serum bilirubin predicts fat-soluble vitamin deficiency better than serum bile acids in infants with biliary atresia.
Academic Article	Intestinal lesions are associated with altered intestinal microbiome and are more frequent in children and young adults with cystic fibrosis and cirrhosis.
Academic Article	Oral fructose absorption in obese children with non-alcoholic fatty liver disease.
Academic Article	Baseline Analysis of a Young a-1-Antitrypsin Deficiency Liver Disease Cohort Reveals Frequent Portal Hypertension.
Academic Article	Quality of Life and Its Determinants in a Multicenter Cohort of Children with Alagille Syndrome.
Academic Article	Portopulmonary Hypertension: Opportunities for Precision Pediatrics.
Academic Article	Intestinal Microbiota, Lipids, and the Pathogenesis of Intestinal Failure-Associated Liver Disease.
Academic Article	Baseline Ultrasound and Clinical Correlates in Children with Cystic Fibrosis.
Award or Honor Receipt	Career Teaching Scholar Award, Department of Pediatrics
Award or Honor Receipt	Fellow of AASLD
Academic Article	Total Serum Bilirubin within 3 Months of Hepatoportoenterostomy Predicts Short-Term Outcomes in Biliary Atresia.
Academic Article	Molecular Chaperones as Therapy for PFIC: Not So Fast!
Academic Article	Early life predictive markers of liver disease outcome in an International, Multicentre Cohort of children with Alagille syndrome.
Academic Article	International Liver Transplant Society Practice Guidelines: Diagnosis and Management of Hepatopulmonary Syndrome and Portopulmonary Hypertension.
Academic Article	Nocturnal hypoxia-induced oxidative stress promotes progression of pediatric non-alcoholic fatty liver disease.
Academic Article	Biliary atresia and other cholestatic childhood diseases: Advances and future challenges.
Academic Article	Newborn Screening for Biliary Atresia: Bilirubin or Bust?
Academic Article	Biliary atresia: Indications and timing of liver transplantation and optimization of pretransplant care.
Academic Article	Neonatal Cholestasis.
Academic Article	A New Old Treatment for Vitamin E Deficiency in Cholestasis.
Academic Article	Alpha-1-Antitrypsin Deficiency: An Important Cause of Pediatric Liver Disease.
Academic Article	Analysis of surgical interruption of the enterohepatic circulation as a treatment for pediatric cholestasis.
Academic Article	Lactate and Lactate: Pyruvate Ratio in the Diagnosis and Outcomes of Pediatric Acute Liver Failure.
Academic Article	Prevalence of elevated liver enzymes in children with cystic fibrosis diagnosed by newborn screen.
Grant	Colorado Clinical and Translational Sciences Institute
Grant	Colorado Clinical and Translational Sciences Institute
Grant	Institutional Training Grant in Pediatric Gastroenterology
Grant	Colorado Center of Childhood Liver Disease Research Network
Grant	Colorado Clinical and Translational Sciences Institute
Award or Honor Receipt	President
Academic Article	Cross-sectional analysis of health-related quality of life in pediatric liver transplant recipients.
Academic Article	Newborn Screening for Biliary Atresia.
Academic Article	Health status of children alive 10 years after pediatric liver transplantation performed in the US and Canada: report of the studies of pediatric liver transplantation experience.
Academic Article	Outcomes of 5-year survivors of pediatric liver transplantation: report on 461 children from a north american multicenter registry.
Academic Article	PedsQL™ Cognitive Functioning Scale in pediatric liver transplant recipients: feasibility, reliability, and validity.
Academic Article	Initial assessment of the infant with neonatal cholestasis-Is this biliary atresia?
Academic Article	Neurodevelopmental Outcome of Young Children with Biliary Atresia and Native Liver: Results from the ChiLDReN Study.
Academic Article	Hepatopulmonary Syndrome and Portopulmonary Hypertension in Children: Recent Advances in Diagnosis and Management.
Academic Article	Biliary Atresia: Clinical and Research Challenges for the Twenty-First Century.
Academic Article	Macrophage-derived IL-1ß/NF-?B signaling mediates parenteral nutrition-associated cholestasis.
Grant	Colorado Clinical and Transational Sciences Institute
Academic Article	Treating Obstructive Sleep Apnea and Chronic Intermittent Hypoxia Improves the Severity of Nonalcoholic Fatty Liver Disease in Children.
Academic Article	TRAPPC11 and GOSR2 mutations associate with hypoglycosylation of a-dystroglycan and muscular dystrophy.
Academic Article	Bone Density in Children With Chronic Liver Disease Correlates With Growth and Cholestasis.
Academic Article	Impact of Steroid Therapy on Early Growth in Infants with Biliary Atresia: The Multicenter Steroids in Biliary Atresia Randomized Trial.
Academic Article	Placebo-Controlled Randomized Trial of an Intestinal Bile Salt Transport Inhibitor for Pruritus in Alagille Syndrome.
Academic Article	Identification of Polycystic Kidney Disease 1 Like 1 Gene Variants in Children With Biliary Atresia Splenic Malformation Syndrome.
Academic Article	Neonatal cholestasis: emerging molecular diagnostics and potential novel therapeutics.
Academic Article	A Phase I/IIa Trial of Intravenous Immunoglobulin Following Portoenterostomy in Biliary Atresia.
Concept	Observational Studies as Topic
Concept	Serrate-Jagged Proteins
Concept	Whole Exome Sequencing
Concept	Self Report
Concept	Fetal Alcohol Spectrum Disorders
Concept	End Stage Liver Disease
Concept	High-Throughput Nucleotide Sequencing
Concept	Heterotaxy Syndrome
Concept	Non-alcoholic Fatty Liver Disease
Academic Article	Noncirrhotic portal hypertension in the pediatric population.
Academic Article	Correlation of Immune Markers With Outcomes in Biliary Atresia Following Intravenous Immunoglobulin Therapy.
Academic Article	Nocturnal Hypoxia Activation of the Hedgehog Signaling Pathway Affects Pediatric Nonalcoholic Fatty Liver Disease Severity.
Academic Article	Neurodevelopmental Outcomes in Preschool and School Aged Children With Biliary Atresia and Their Native Liver.
Academic Article	Up-regulation of miR-let7a-5p Leads to Decreased Expression of ABCC2 in Obstructive Cholestasis.
Grant	Rare Liver Disease Network
Grant	Colorado Clinical and Translational Science Institute (KL2)
Grant	Colorado Clinical and Translational Science Institute (TL1)
Grant	Colorado Clinical and Translational Science Institute (KL2)
Grant	Oxidant Hepatic Injury in Cholestasis
Grant	Colorado Clinical and Translational Science Institute (UL1)
Grant	Rare Liver Disease Network
Grant	Colorado Clinical and Translational Science Institute (TL1)
Grant	Colorado Clinical and Translational Science Institute (UL1)
Grant	EFFECT OF VITAMIN E ON HEPATOCYTE STRUCTURE AND FUNCTION
Academic Article	New Insights Into Intestinal Failure-Associated Liver Disease in Children.
Academic Article	Mitochondrial disease disrupts hepatic allostasis and lowers the threshold for immune-mediated liver toxicity.
Academic Article	Intestinal failure-associated liver disease (IFALD): insights into pathogenesis and advances in management.
Academic Article	Erythrocyte autoantibodies, autoimmune haemolysis, and myelodysplastic syndromes.
Academic Article	Reopening Schools Safely: The Case for Collaboration, Constructive Disruption of Pre-Coronavirus 2019 Expectations, and Creative Solutions.
Academic Article	Unraveling the Relationship Between Itching, Scratch Scales, and Biomarkers in Children With Alagille Syndrome.
Academic Article	Longitudinal Outcomes in Young Patients with Alpha-1-Antitrypsin Deficiency with Native Liver Reveal that Neonatal Cholestasis is a Poor Predictor of Future Portal Hypertension.
Academic Article	Recent developments in diagnostics and treatment of neonatal cholestasis.
Academic Article	Modeling Outcomes in Children With Biliary Atresia With Native Liver After 2 Years of Age.
Academic Article	Outcomes of Childhood Cholestasis in Alagille Syndrome: Results of a Multicenter Observational Study.
Academic Article	Nonfasted Liver Stiffness Correlates with Liver Disease Parameters and Portal Hypertension in Pediatric Cholestatic Liver Disease.
Academic Article	Impact of Genotype, Serum Bile Acids, and Surgical Biliary Diversion on Native Liver Survival in FIC1 Deficiency.
Academic Article	Use of a Comprehensive 66-Gene Cholestasis Sequencing Panel in 2171 Cholestatic Infants, Children, and Young Adults.
Academic Article	Mutation Analysis and Disease Features at Presentation in a Multi-Center Cohort of Children With Monogenic Cholestasis.
Academic Article	The clinical utility of maternal body mass index in pregnancy.
Academic Article	Malnutrition in Biliary Atresia: Assessment, Management, and Outcomes.
Academic Article	Fostering innovation at Academic Medical Centers: The Case of University of Colorado Anschutz Medical Campus.
Academic Article	NF-?B Regulation of LRH-1 and ABCG5/8 Potentiates Phytosterol Role in the Pathogenesis of Parenteral Nutrition-Associated Cholestasis.
Academic Article	What affects fetal pulmonary maturation during diabetic pregnancy?
Academic Article	Interrupting tumor necrosis factor-alpha signaling prevents parenteral nutrition-associated cholestasis in mice.
Academic Article	Presentation and Outcomes of Infants With Idiopathic Cholestasis: A Multicenter Prospective Study.
Academic Article	Pharmacologic Activation of Hepatic Farnesoid X Receptor Prevents Parenteral Nutrition Associated Cholestasis in Mice.
Academic Article	Limitations of using maximum vertical pocket and other sonographic evaluations of amniotic fluid volume to predict fetal growth: technical or physiologic?
Academic Article	Neurodevelopmental Outcomes in Children with Inherited Liver Disease and Native Liver.
Academic Article	Alcohol teratogenicity in the human: a detailed assessment of specificity, critical period, and threshold.
Academic Article	A modified lecithin/sphingomyelin ratio test for fetal maturity.
Academic Article	Maternal and fetal circulating levels of thymosin alpha 1 during parturition.

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