 Familial Primary Pulmonary Hypertension
"Familial Primary Pulmonary Hypertension" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
Familial or idiopathic hypertension in the PULMONARY CIRCULATION which is not secondary to other disease.
| Descriptor ID |
D065627
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| MeSH Number(s) |
C08.381.423.847
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| Concept/Terms |
Idiopathic Pulmonary Arterial Hypertension- Idiopathic Pulmonary Arterial Hypertension
- Primary Pulmonary Hypertension
- Hypertension, Primary Pulmonary
- Hypertensions, Primary Pulmonary
- Primary Pulmonary Hypertensions
- Pulmonary Hypertension, Primary
- Pulmonary Hypertensions, Primary
- Pulmonary Hypertension, Primary, 1
- Idiopathic Pulmonary Hypertension
- Hypertension, Idiopathic Pulmonary
- Hypertensions, Idiopathic Pulmonary
- Idiopathic Pulmonary Hypertensions
- Pulmonary Hypertension, Idiopathic
- Pulmonary Hypertensions, Idiopathic
Pulmonary Hypertension, Primary, 1, With Hereditary Hemorrhagic Telangiectasia- Pulmonary Hypertension, Primary, 1, With Hereditary Hemorrhagic Telangiectasia
- Pph1 With Hht
- Hht, Pph1 With
- Hhts, Pph1 With
- Pph1 With Hhts
- With Hht, Pph1
- With Hhts, Pph1
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Below are MeSH descriptors whose meaning is more general than "Familial Primary Pulmonary Hypertension".
Below are MeSH descriptors whose meaning is more specific than "Familial Primary Pulmonary Hypertension".
This graph shows the total number of publications written about "Familial Primary Pulmonary Hypertension" by people in this website by year, and whether "Familial Primary Pulmonary Hypertension" was a major or minor topic of these publications.
To see the data from this visualization as text, click here.
| Year | Major Topic | Minor Topic | Total |
|---|
| 2010 | 0 | 2 | 2 | | 2011 | 0 | 16 | 16 | | 2012 | 0 | 15 | 15 | | 2013 | 0 | 17 | 17 | | 2014 | 0 | 11 | 11 | | 2015 | 2 | 0 | 2 | | 2016 | 6 | 1 | 7 | | 2017 | 1 | 2 | 3 | | 2018 | 3 | 2 | 5 | | 2019 | 1 | 2 | 3 | | 2020 | 0 | 2 | 2 | | 2021 | 1 | 6 | 7 | | 2022 | 0 | 12 | 12 | | 2023 | 0 | 9 | 9 | | 2024 | 0 | 2 | 2 |
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Below are the most recent publications written about "Familial Primary Pulmonary Hypertension" by people in Profiles.
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Ploegstra MJ, Ivy DD, Beghetti M, Bonnet D, Alehan D, Ablonczy L, Mattos S, Bowers D, Humpl T, Berger RMF. Long-term outcome of children with newly diagnosed pulmonary arterial hypertension: results from the global TOPP registry. Eur Heart J Qual Care Clin Outcomes. 2024 Jan 12; 10(1):66-76.
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Neves da Silva HV, Weinman JP, Englund EK, Deterding RR, Ivy DD, Browne LP. Computed tomographic findings in TBX4 mutation: a common cause of severe pulmonary artery hypertension in children. Pediatr Radiol. 2024 02; 54(2):199-207.
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Doughty ES, Norvik C, Levin A, Bodmer J, Tran-Lundmark K, Abman SH, Galambos C. Long-Term Effect of TBX4 Germline Mutation on Pulmonary Clinico-Histopathologic Phenotype. Pediatr Dev Pathol. 2024 Jan-Feb; 27(1):83-89.
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Souza R, Badesch DB, Ghofrani HA, Gibbs JSR, Gomberg-Maitland M, McLaughlin VV, Preston IR, Waxman AB, Gr?nig E, Kopec G, Meyer G, Olsson KM, Rosenkranz S, Lin J, Johnson-Levonas AO, de Oliveira Pena J, Humbert M, Hoeper MM. Effects of sotatercept on haemodynamics and right heart function: analysis of the STELLAR trial. Eur Respir J. 2023 09; 62(3).
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Avitabile CM, Yung D, Handler S, Hopper RK, Fineman J, Freire G, Varghese N, Mullen MP, Krishnan US, Austin E, Silveira L, Ivy DD. Measurement of Physical Activity by Actigraphy in Infants and Young Children with Pulmonary Arterial Hypertension. J Pediatr. 2023 11; 262:113639.
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McCormick A, Krishnan A, Badesch D, Benza RL, Bull TM, De Marco T, Feldman J, Hemnes AR, Hirsch R, Horn E, Kennedy J, Mathai SC, McConnell W, Pugliese SC, Sager JS, Shlobin OA, Simon MA, Lammi MR. Pulmonary artery compliance in different forms of pulmonary hypertension. Heart. 2023 06 26; 109(14):1098-1105.
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Chakraborty A, Nathan A, Orcholski M, Agarwal S, Shamskhou EA, Auer N, Mitra A, Guardado ES, Swaminathan G, Condon DF, Yu J, McCarra M, Juul NH, Mallory A, Guzman-Hernandez RA, Yuan K, Rojas V, Crossno JT, Yung LM, Yu PB, Spencer T, Winn RA, Frump A, Karoor V, Lahm T, Hedlin H, Fineman JR, Lafyatis R, Knutsen CNF, Alvira CM, Cornfield DN, de Jesus Perez VA. Wnt7a deficit is associated with dysfunctional angiogenesis in pulmonary arterial hypertension. Eur Respir J. 2023 06; 61(6).
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Sangam S, Sun X, Schwantes-An TH, Yegambaram M, Lu Q, Shi Y, Cook T, Fisher A, Frump AL, Coleman A, Sun Y, Liang S, Crawford H, Lutz KA, Maun AD, Pauciulo MW, Karnes JH, Chaudhary KR, Stewart DJ, Langlais PR, Jain M, Alotaibi M, Lahm T, Jin Y, Gu H, Tang H, Nichols WC, Black SM, Desai AA. SOX17 Deficiency Mediates Pulmonary Hypertension: At the Crossroads of Sex, Metabolism, and Genetics. Am J Respir Crit Care Med. 2023 04 15; 207(8):1055-1069.
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Brown CE, Steiner JM, Modes M, Lynch Y, Leary PJ, Curtis JR, Engelberg RA. Palliative Care Perspectives of Patients with Pulmonary Arterial Hypertension. Ann Am Thorac Soc. 2023 02; 20(2):331-334.
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Humbert M, McLaughlin V, Gibbs JSR, Gomberg-Maitland M, Hoeper MM, Preston IR, Souza R, Waxman AB, Ghofrani HA, Escribano Subias P, Feldman J, Meyer G, Montani D, Olsson KM, Manimaran S, de Oliveira Pena J, Badesch DB. Sotatercept for the treatment of pulmonary arterial hypertension: PULSAR open-label extension. Eur Respir J. 2023 01; 61(1).
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