Item Type | Name |
Award or Honor Receipt
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Pediatric Liver Research Award,
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Academic Article
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Vitamin E deficiency in adults with chronic liver disease.
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Academic Article
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Orthotopic liver transplantation for acute fulminant Wilson disease.
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Academic Article
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Grade I Reye's syndrome. A frequent cause of vomiting and liver dysfunction after varicella and upper-respiratory-tract infection.
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Academic Article
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Outcome of syndromic paucity of interlobular bile ducts (Alagille syndrome) with onset of cholestasis in infancy.
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Academic Article
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Oxidant injury to hepatic mitochondria in patients with Wilson's disease and Bedlington terriers with copper toxicosis.
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Academic Article
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Association of paucity of interlobular bile ducts with prune belly syndrome.
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Academic Article
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Abnormal hepatic mitochondrial respiration and cytochrome C oxidase activity in rats with long-term copper overload.
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Academic Article
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Hepatic concentrations of zinc, copper and manganese in infants with extrahepatic biliary atresia.
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Academic Article
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Antioxidant defenses in metal-induced liver damage.
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Academic Article
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Vitamin E reduces oxidant injury to mitochondria and the hepatotoxicity of taurochenodeoxycholic acid in the rat.
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Academic Article
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Total parenteral nutrition-related liver disease.
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Academic Article
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Effect of oxypurinol, a xanthine oxidase inhibitor, on hepatic injury in the bile duct-ligated rat.
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Academic Article
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Effect of ursodeoxycholic acid therapy on hepatic function in children with intrahepatic cholestatic liver disease.
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Academic Article
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Fat-soluble vitamins and their importance in patients with cholestatic liver diseases.
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Academic Article
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Mitochondria and childhood liver diseases.
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Academic Article
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Recommendations for management of liver and biliary tract disease in cystic fibrosis. Cystic Fibrosis Foundation Hepatobiliary Disease Consensus Group.
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Academic Article
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Correction of hypozincemia following liver transplantation in children is associated with reduced urinary zinc loss.
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Academic Article
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The effect of idebenone, a coenzyme Q analogue, on hydrophobic bile acid toxicity to isolated rat hepatocytes and hepatic mitochondria.
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Academic Article
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Disorders of the mitochondria.
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Academic Article
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Identification of a new inborn error in bile acid synthesis: mutation of the oxysterol 7alpha-hydroxylase gene causes severe neonatal liver disease.
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Academic Article
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At long last: an animal model of Wilson's disease.
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Academic Article
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Evidence for involvement of oxygen free radicals in bile acid toxicity to isolated rat hepatocytes.
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Academic Article
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Liver disease in Navajo neuropathy.
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Academic Article
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Liver transplantation in mitochondrial respiratory chain disorders.
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Academic Article
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Fulminant hepatitis associated with centrilobular hepatic necrosis in young children.
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Academic Article
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Long-term results with the Kasai operation for biliary atresia.
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Academic Article
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Hepatoblastoma in a neonate: a hypervascular presentation mimicking hemangioendothelioma.
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Academic Article
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Biliary atresia: current concepts and research directions. Summary of a symposium.
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Academic Article
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alpha-tocopherol ameliorates oxidant injury in isolated copper-overloaded rat hepatocytes.
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Academic Article
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Navajo neurohepatopathy: a mitochondrial DNA depletion syndrome?
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Academic Article
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Cholangiocyte biology and cystic fibrosis liver disease.
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Academic Article
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Nitric oxide ameliorates hydrophobic bile acid-induced apoptosis in isolated rat hepatocytes by non-mitochondrial pathways.
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Academic Article
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Introduction to the pediatric liver research agenda: a blueprint for the future.
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Academic Article
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Variability of biochemical and clinical phenotype in X-linked liver glycogenosis with mutations in the phosphorylase kinase PHKA2 gene.
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Academic Article
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Case report: nonalcoholic steatohepatitis in a teenage girl with type 2 diabetes.
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Academic Article
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Gastrointestinal manifestations of mitochondrial disease.
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Academic Article
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Biliary atresia is associated with CD4+ Th1 cell-mediated portal tract inflammation.
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Academic Article
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Liver involvement in Alpers disease.
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Academic Article
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Beta-carotene prevents bile acid-induced cytotoxicity in the rat hepatocyte: Evidence for an antioxidant and anti-apoptotic role of beta-carotene in vitro.
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Academic Article
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Portopulmonary hypertension in pediatric patients.
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Academic Article
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Human hepatic mitochondria generate reactive oxygen species and undergo the permeability transition in response to hydrophobic bile acids.
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Academic Article
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Characterization of acute liver failure and development of a continuous risk of death staging system in children.
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Academic Article
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Armed CD4+ Th1 effector cells and activated macrophages participate in bile duct injury in murine biliary atresia.
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Academic Article
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Biliary atresia: clinical profiles, risk factors, and outcomes of 755 patients listed for liver transplantation.
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Academic Article
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Comparison of indices of vitamin A status in children with chronic liver disease.
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Academic Article
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Connective tissue growth factor expression is increased in biliary epithelial cells in biliary atresia.
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Academic Article
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Acute hepatitis and liver failure associated with influenza A infection in children.
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Academic Article
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Subcutaneous vitamin E ameliorates liver injury in an in vivo model of steatocholestasis.
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Academic Article
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Screening and outcomes in biliary atresia: summary of a National Institutes of Health workshop.
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Academic Article
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Liver disease in mitochondrial disorders.
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Academic Article
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Oligoclonal expansions of CD4+ and CD8+ T-cells in the target organ of patients with biliary atresia.
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Academic Article
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Impaired ability of patients with familial isolated vitamin E deficiency to incorporate alpha-tocopherol into lipoproteins secreted by the liver.
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Academic Article
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Anthropometric evaluation of children with chronic liver disease.
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Academic Article
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Hepatic veno-occlusive disease and human herpes virus 7 infection in primary agammaglobulinemia.
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Academic Article
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Biliary atresia screening: why, when, and how?
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Academic Article
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Treatment of neonatal hemochromatosis with exchange transfusion and intravenous immunoglobulin.
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Academic Article
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Reloading against rare liver diseases.
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Academic Article
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Pulmonary vascular complications in asymptomatic children with portal hypertension.
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Academic Article
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Glutathione status of isolated rat hepatocytes affects bile acid-induced cellular necrosis but not apoptosis.
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Academic Article
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Design and validation of the biliary atresia research consortium histologic assessment system for cholestasis in infancy.
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Academic Article
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The chronic disease of childhood obesity: the sleeping giant has awakened.
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Academic Article
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The anatomic pattern of biliary atresia identified at time of Kasai hepatoportoenterostomy and early postoperative clearance of jaundice are significant predictors of transplant-free survival
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Academic Article
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American Liver Foundation releases Pediatric Liver Research Agenda-2000.
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Academic Article
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Liver cell injury and fibrosis.
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Academic Article
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Portal hypertension in children and young adults with biliary atresia.
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Academic Article
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Lack of correlation between infection with reovirus 3 and extrahepatic biliary atresia or neonatal hepatitis.
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Academic Article
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Clues to the etiology of bile duct injury in biliary atresia.
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Academic Article
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Copper toxicity and lipid peroxidation in isolated rat hepatocytes: effect of vitamin E.
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Academic Article
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Medical management of the infant or child with chronic liver disease.
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Academic Article
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Correction of vitamin E deficiency in children with chronic cholestasis. II. Effect on gastrointestinal and hepatic function.
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Academic Article
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New North American research network focuses on biliary atresia and neonatal liver disease.
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Academic Article
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Hepatic dysfunction following the Fontan procedure.
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Academic Article
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Effect of dietary lipid and vitamin E on mitochondrial lipid peroxidation and hepatic injury in the bile duct-ligated rat.
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Academic Article
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Vitamin E deficiency in cholestatic liver disease.
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Academic Article
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Generation of hydroperoxides in isolated rat hepatocytes and hepatic mitochondria exposed to hydrophobic bile acids.
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Academic Article
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Biliary diversion for progressive familial intrahepatic cholestasis: improved liver morphology and bile acid profile.
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Academic Article
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Interferon treatment for chronic hepatitis B: enhanced response in children 5 years old or younger.
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Academic Article
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Hepatic oxidant injury and glutathione depletion during total parenteral nutrition in weanling rats.
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Academic Article
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Enrichment of rat hepatic organelles by vitamin E administered subcutaneously.
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Academic Article
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Licorice compounds glycyrrhizin and 18beta-glycyrrhetinic acid are potent modulators of bile acid-induced cytotoxicity in rat hepatocytes.
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Academic Article
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Unraveling the pathogenesis and etiology of biliary atresia.
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Academic Article
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Increased susceptibility of fat-laden Zucker-rat hepatocytes to bile acid-induced oncotic necrosis: an in vitro model of steatocholestasis.
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Academic Article
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Fulminant Epstein-Barr viral hepatitis: orthotopic liver transplantation and review of the literature.
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Academic Article
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Hepato-portopulmonary disorders--not just in adults!
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Academic Article
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Acute liver failure in children: the first 348 patients in the pediatric acute liver failure study group.
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Academic Article
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Health-related quality of life in pediatric liver transpant recipients compared to other chronic disease groups
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Academic Article
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Outcomes in children who underwent transplantation for autoimmune hepatitis
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Academic Article
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"Let there be bile"--understanding hepatic injury in cholestasis.
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Academic Article
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Role of oxidant stress in the permeability transition induced in rat hepatic mitochondria by hydrophobic bile acids.
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Academic Article
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Improvement of cyclosporin absorption in children after liver transplantation by means of water-soluble vitamin E.
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Academic Article
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Etiopathogenesis of biliary atresia.
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Academic Article
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Hepatobiliary disease in neonatal lupus: prevalence and clinical characteristics in cases enrolled in a national registry.
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Academic Article
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Niemann-pick disease type C in neonatal cholestasis at a North American Center.
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Academic Article
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Autoantibodies in mothers of children with neonatal liver disease.
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Academic Article
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Quantitation of rat liver vitamin E metabolites by LC-MS during high-dose vitamin E administration.
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Academic Article
|
Mitochondrial hepatopathies: advances in genetics and pathogenesis.
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Academic Article
|
Growth failure and outcomes in infants with biliary atresia: a report from the Biliary Atresia Research Consortium.
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Academic Article
|
Alpha-tocopherol regulation of hepatic cytochrome P450s and ABC transporters in rats.
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Academic Article
|
Evaluation of a scoring system for assessing prognosis in pediatric acute liver failure.
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Academic Article
|
Effect of vitamin E on transport processes in isolated rat hepatocytes.
|
Academic Article
|
Failure of resolution of portal fibrosis during omega-3 fatty acid lipid emulsion therapy in two patients with irreversible intestinal failure.
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Academic Article
|
Mechanisms of disease: Inborn errors of bile acid synthesis.
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Academic Article
|
Resistance of young rat hepatic mitochondria to bile acid-induced permeability transition: potential role of alpha-tocopherol.
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Academic Article
|
Cardiopulmonary manifestations of portovenous shunts from congenital absence of the portal vein: pulmonary hypertension and pulmonary vascular dilatation.
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Academic Article
|
Oxidant injury to hepatic mitochondrial lipids in rats with dietary copper overload. Modification by vitamin E deficiency.
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Academic Article
|
Choledochoduodenostomy in pediatric liver transplantation.
|
Academic Article
|
Parenteral nutrition supplementation in biliary atresia patients listed for liver transplantation.
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Academic Article
|
Intestinal malabsorption of vitamin E in primary biliary cirrhosis.
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Academic Article
|
Toll-like receptor 4-dependent Kupffer cell activation and liver injury in a novel mouse model of parenteral nutrition and intestinal injury.
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Academic Article
|
Pulmonary function in individuals who underwent liver transplantation: from the US cystic fibrosis foundation registry.
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Academic Article
|
Evaluation of the liver injury unit scoring system to predict survival in a multinational study of pediatric acute liver failure.
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Concept
|
Liver Diseases
|
Concept
|
Liver Cirrhosis
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Concept
|
Liver
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Concept
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Liver Extracts
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Concept
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Liver Cirrhosis, Biliary
|
Concept
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Liver Transplantation
|
Concept
|
Liver Function Tests
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Concept
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Chemical and Drug Induced Liver Injury
|
Concept
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Liver Failure
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Concept
|
Fatty Liver
|
Concept
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Liver Cirrhosis, Experimental
|
Concept
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Liver Failure, Acute
|
Concept
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Liver Diseases, Alcoholic
|
Concept
|
Liver Glycogen
|
Concept
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Mitochondria, Liver
|
Concept
|
Liver Neoplasms
|
Concept
|
Microsomes, Liver
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Award or Honor Receipt
|
Governing Board
|
Academic Article
|
Phytosterols promote liver injury and Kupffer cell activation in parenteral nutrition-associated liver disease.
|
Academic Article
|
Health related quality of life in patients with biliary atresia surviving with their native liver.
|
Academic Article
|
Evaluation of the child with suspected mitochondrial liver disease.
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Academic Article
|
Mitochondrial hepatopathies: advances in genetics, therapeutic approaches, and outcomes.
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Academic Article
|
Obstructive sleep apnea and hypoxemia are associated with advanced liver histology in pediatric nonalcoholic fatty liver disease.
|
Academic Article
|
Significant hepatic involvement in patients with ornithine transcarbamylase deficiency.
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Academic Article
|
Liver transplantation for pediatric metabolic disease.
|
Academic Article
|
Mutations in TJP2 cause progressive cholestatic liver disease.
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Academic Article
|
Medical status of 219 children with biliary atresia surviving long-term with their native livers: results from a North American multicenter consortium.
|
Academic Article
|
Specific microbiome changes in a mouse model of parenteral nutrition associated liver injury and intestinal inflammation.
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Academic Article
|
Intestinal lesions are associated with altered intestinal microbiome and are more frequent in children and young adults with cystic fibrosis and cirrhosis.
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Academic Article
|
Oral fructose absorption in obese children with non-alcoholic fatty liver disease.
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Academic Article
|
Baseline Analysis of a Young a-1-Antitrypsin Deficiency Liver Disease Cohort Reveals Frequent Portal Hypertension.
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Academic Article
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Portopulmonary Hypertension: Opportunities for Precision Pediatrics.
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Academic Article
|
Intestinal Microbiota, Lipids, and the Pathogenesis of Intestinal Failure-Associated Liver Disease.
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Academic Article
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Baseline Ultrasound and Clinical Correlates in Children with Cystic Fibrosis.
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Award or Honor Receipt
|
Fellow of AASLD
|
Academic Article
|
Total Serum Bilirubin within 3 Months of Hepatoportoenterostomy Predicts Short-Term Outcomes in Biliary Atresia.
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Academic Article
|
Early life predictive markers of liver disease outcome in an International, Multicentre Cohort of children with Alagille syndrome.
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Academic Article
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International Liver Transplant Society Practice Guidelines: Diagnosis and Management of Hepatopulmonary Syndrome and Portopulmonary Hypertension.
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Academic Article
|
Nocturnal hypoxia-induced oxidative stress promotes progression of pediatric non-alcoholic fatty liver disease.
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Academic Article
|
Biliary atresia: Indications and timing of liver transplantation and optimization of pretransplant care.
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Academic Article
|
Alpha-1-Antitrypsin Deficiency: An Important Cause of Pediatric Liver Disease.
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Academic Article
|
Lactate and Lactate: Pyruvate Ratio in the Diagnosis and Outcomes of Pediatric Acute Liver Failure.
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Academic Article
|
Prevalence of elevated liver enzymes in children with cystic fibrosis diagnosed by newborn screen.
|
Grant
|
Colorado Center of Childhood Liver Disease ResearchNetwork
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Award or Honor Receipt
|
President
|
Academic Article
|
Cross-sectional analysis of health-related quality of life in pediatric liver transplant recipients.
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Academic Article
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Health status of children alive 10 years after pediatric liver transplantation performed in the US and Canada: report of the studies of pediatric liver transplantation experience.
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Academic Article
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Outcomes of 5-year survivors of pediatric liver transplantation: report on 461 children from a north american multicenter registry.
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Academic Article
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PedsQL? Cognitive Functioning Scale in pediatric liver transplant recipients: feasibility, reliability, and validity.
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Academic Article
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Neurodevelopmental Outcome of Young Children with Biliary Atresia and Native Liver: Results from the ChiLDReN Study.
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Academic Article
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Hepatopulmonary Syndrome and Portopulmonary Hypertension in Children: Recent Advances in Diagnosis and Management.
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Academic Article
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Macrophage-derived IL-1?/NF-?B signaling mediates parenteral nutrition-associated cholestasis.
|
Academic Article
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Treating Obstructive Sleep Apnea and Chronic Intermittent Hypoxia Improves the Severity of Nonalcoholic Fatty Liver Disease in Children.
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Academic Article
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Bone Density in Children With Chronic Liver Disease Correlates With Growth and Cholestasis.
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Academic Article
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A Phase I/IIa Trial of Intravenous Immunoglobulin Following Portoenterostomy in Biliary Atresia.
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Concept
|
Liver X Receptors
|
Concept
|
End Stage Liver Disease
|
Concept
|
Non-alcoholic Fatty Liver Disease
|
Academic Article
|
Noncirrhotic portal hypertension in the pediatric population.
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Academic Article
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Nocturnal Hypoxia Activation of the Hedgehog Signaling Pathway Affects Pediatric Nonalcoholic Fatty Liver Disease Severity.
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Academic Article
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Neurodevelopmental Outcomes in Preschool and School Aged Children With Biliary Atresia and Their Native Liver.
|
Grant
|
Rare Liver Disease Network
|
Grant
|
Oxidant Hepatic Injury in Cholestasis
|
Grant
|
Rare Liver Disease Network
|
Grant
|
EFFECT OF VITAMIN E ON HEPATOCYTE STRUCTURE AND FUNCTION
|
Academic Article
|
New Insights Into Intestinal Failure-Associated Liver Disease in Children.
|
Academic Article
|
Mitochondrial disease disrupts hepatic allostasis and lowers the threshold for immune-mediated liver toxicity.
|
Academic Article
|
Intestinal failure-associated liver disease (IFALD): insights into pathogenesis and advances in management.
|
Academic Article
|
Longitudinal Outcomes in Young Patients with Alpha-1-Antitrypsin Deficiency with Native Liver Reveal that Neonatal Cholestasis is a Poor Predictor of Future Portal Hypertension.
|
Academic Article
|
Modeling Outcomes in Children With Biliary Atresia With Native Liver After 2 Years of Age.
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Academic Article
|
Nonfasted Liver Stiffness Correlates with Liver Disease Parameters and Portal Hypertension in Pediatric Cholestatic Liver Disease.
|
Academic Article
|
Impact of Genotype, Serum Bile Acids, and Surgical Biliary Diversion on Native Liver Survival in FIC1 Deficiency.
|
Academic Article
|
Malnutrition in Biliary Atresia: Assessment, Management, and Outcomes.
|
Academic Article
|
Pharmacologic activation of hepatic farnesoid X receptor prevents parenteral nutrition-associated cholestasis in mice.
|
Academic Article
|
Neurodevelopmental Outcomes in Children With Inherited Liver Disease and Native Liver.
|
Academic Article
|
Neonatal Cholestasis: Updates on Diagnostics, Therapeutics, and Prevention.
|
Award or Honor Receipt
|
Peak of Excellence Award
|
Award or Honor Receipt
|
2020 Sass-Kortsak Award
|
Academic Article
|
Use of funded multicenter prospective longitudinal databases to inform clinical trials in rare diseases-Examination of cholestatic liver disease in Alagille syndrome.
|
Academic Article
|
Fat Soluble Vitamin Assessment and Supplementation in Cholestasis.
|
Academic Article
|
Macronutrient and Micronutrient Intake in Adolescents With Non-alcoholic Fatty Liver Disease: The Association With Disease Severity.
|
Academic Article
|
Thioredoxin reductase 1 regulates hepatic inflammation and macrophage activation during acute cholestatic liver injury.
|
Academic Article
|
The autophagic protein p62 is a target of reactive aldehydes in human and murine cholestatic liver disease.
|
Academic Article
|
Serum biomarkers correlated with liver stiffness assessed in a multicenter study of pediatric cholestatic liver disease.
|
Academic Article
|
The discriminatory ability of FibroScan liver stiffness measurement, controlled attenuation parameter, and FibroScan-aspartate aminotransferase to predict severity of liver disease in children.
|
Academic Article
|
Pharmacologic inhibition of HNF4a prevents parenteral nutrition associated cholestasis in mice.
|
Academic Article
|
Clinical spectrum and genetic causes of mitochondrial hepatopathy phenotype in children.
|
Academic Article
|
Cytomegalovirus in biliary atresia is associated with increased pretransplant death, but not decreased native liver survival.
|
Academic Article
|
Sarcopenia is associated with osteopenia and impaired quality of life in children with genetic intrahepatic cholestatic liver disease.
|
Academic Article
|
Neonatal cholestasis in children with Alpha-1-AT deficiency is a risk for earlier severe liver disease with male predominance.
|
Academic Article
|
Protein biomarkers GDF15 and FGF21 to differentiate mitochondrial hepatopathies from other pediatric liver diseases.
|