 Idiopathic Pulmonary Fibrosis
"Idiopathic Pulmonary Fibrosis" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
| Descriptor ID |
D054990
|
| MeSH Number(s) |
C08.381.483.487.500 C08.381.765.500
|
| Concept/Terms |
Idiopathic Pulmonary Fibrosis- Idiopathic Pulmonary Fibrosis
- Idiopathic Pulmonary Fibroses
- Pulmonary Fibroses, Idiopathic
- Familial Idiopathic Pulmonary Fibrosis
- Fibrocystic Pulmonary Dysplasia
- Dysplasia, Fibrocystic Pulmonary
- Dysplasias, Fibrocystic Pulmonary
- Fibrocystic Pulmonary Dysplasias
- Pulmonary Dysplasia, Fibrocystic
- Pulmonary Dysplasias, Fibrocystic
- Fibrosing Alveolitis, Cryptogenic
- Hamman-Rich Disease
- Disease, Hamman-Rich
- Diseases, Hamman-Rich
- Hamman Rich Disease
- Hamman-Rich Diseases
- Interstitial Pneumonitis, Usual
- Interstitial Pneumonitides, Usual
- Pneumonitides, Usual Interstitial
- Pneumonitis, Usual Interstitial
- Usual Interstitial Pneumonitides
- Usual Interstitial Pneumonitis
- Pulmonary Fibrosis, Idiopathic
- Usual Interstitial Pneumonia
- Interstitial Pneumonia, Usual
- Interstitial Pneumonias, Usual
- Usual Interstitial Pneumonias
- Idiopathic Fibrosing Alveolitis, Chronic Form
- Cryptogenic Fibrosing Alveolitis
- Cryptogenic Fibrosing Alveolitides
- Fibrosing Alveolitides, Cryptogenic
- Idiopathic Pulmonary Fibrosis, Familial
|
Below are MeSH descriptors whose meaning is more general than "Idiopathic Pulmonary Fibrosis".
Below are MeSH descriptors whose meaning is more specific than "Idiopathic Pulmonary Fibrosis".
This graph shows the total number of publications written about "Idiopathic Pulmonary Fibrosis" by people in this website by year, and whether "Idiopathic Pulmonary Fibrosis" was a major or minor topic of these publications.
To see the data from this visualization as text, click here.
| Year | Major Topic | Minor Topic | Total |
|---|
| 2008 | 1 | 0 | 1 | | 2009 | 10 | 2 | 12 | | 2010 | 4 | 0 | 4 | | 2011 | 12 | 1 | 13 | | 2012 | 15 | 1 | 16 | | 2013 | 15 | 1 | 16 | | 2014 | 19 | 1 | 20 | | 2015 | 24 | 3 | 27 | | 2016 | 19 | 3 | 22 | | 2017 | 28 | 1 | 29 | | 2018 | 22 | 2 | 24 | | 2019 | 23 | 1 | 24 | | 2020 | 15 | 1 | 16 | | 2021 | 21 | 0 | 21 | | 2022 | 31 | 0 | 31 | | 2023 | 27 | 0 | 27 | | 2024 | 17 | 4 | 21 | | 2025 | 5 | 0 | 5 |
To return to the timeline, click here.
Below are the most recent publications written about "Idiopathic Pulmonary Fibrosis" by people in Profiles.
-
Blumhagen RZ, Humphries SM, Peljto AL, Lynch DA, Cardwell J, Bang TJ, Teague SD, Sigakis C, Walts AD, Puthenvedu D, Wolters PJ, Blackwell TS, Kropski JA, Brown KK, Schwarz MI, Yang IV, Steele MP, Schwartz DA, Lee JS. MUC5B Genotype and Other Common Variants Are Associated with Computational Imaging Features of Usual Interstitial Pneumonia. Ann Am Thorac Soc. 2025 Apr; 22(4):533-540.
-
Kam MLW, Tjong ELH, Chaudhary S, Koelsch TL, Pryor JB, Koslow M, Mohning MP, Solomon JJ, Huie TJ, Swigris JJ, Fern?ndez P?rez ER. Development and validation of a clinical, CT, genomic classifier and BAL scoring system for diagnosing idiopathic pulmonary fibrosis. Eur Respir J. 2025 Mar; 65(3).
-
McDermott GC, Moll M, Cho MH, Hayashi K, Juge PA, Doyle TJ, Paudel ML, Kinney GL, Kronzer VL, Kim JS, O'Keeffe LA, Davis NA, Bernstein EJ, Dellaripa PF, Regan EA, Hunninghake GM, Silverman EK, Ash SY, San Jose Estepar R, Washko GR, Sparks JA. Polygenic risk scores for rheumatoid arthritis and idiopathic pulmonary fibrosis and associations with RA, interstitial lung abnormalities, and quantitative interstitial abnormalities among smokers. Semin Arthritis Rheum. 2025 Jun; 72:152708.
-
Dalapati T, Wang L, Jones AG, Cardwell J, Konigsberg IR, Boss? Y, Sin DD, Timens W, Hao K, Yang I, Ko DC. Context-specific eQTLs provide deeper insight into causal genes underlying shared genetic architecture of COVID-19 and idiopathic pulmonary fibrosis. HGG Adv. 2025 Apr 10; 6(2):100410.
-
Bridges JP, Vladar EK, Kurche JS, Krivoi A, Stancil IT, Dobrinskikh E, Hu Y, Sasse SK, Lee JS, Blumhagen RZ, Yang IV, Gerber AN, Peljto AL, Evans CM, Redente EF, Riches DW, Schwartz DA. Progressive lung fibrosis: reprogramming a genetically vulnerable bronchoalveolar epithelium. J Clin Invest. 2025 Jan 02; 135(1).
-
Salisbury ML, Markin C, Fadely T, Guttentag AR, Humphries SM, Lynch DA, Kropski JA, Blackwell TS. Progressive Early Interstitial Lung Abnormalities in Persons at Risk for Familial Pulmonary Fibrosis: A Prospective Cohort Study. Am J Respir Crit Care Med. 2024 Dec 15; 210(12):1441-1452.
-
Xu H, Hui SL, Lee JS, Zhang Z, Boente RD. Effect of Antifibrotic Use on Mortality in Patients with Idiopathic Pulmonary Fibrosis. Ann Am Thorac Soc. 2024 Oct; 21(10):1407-1415.
-
Nathan SD, Lee JS. Real-world data on the course of idiopathic pulmonary fibrosis. Am J Manag Care. 2024 Oct; 30(7 Suppl):S107-S113.
-
Huang Y, Ma SF, Oldham JM, Adegunsoye A, Zhu D, Murray S, Kim JS, Bonham C, Strickland E, Linderholm AL, Lee CT, Paul T, Mannem H, Maher TM, Molyneaux PL, Strek ME, Martinez FJ, Noth I. Machine Learning of Plasma Proteomics Classifies Diagnosis of Interstitial Lung Disease. Am J Respir Crit Care Med. 2024 Aug 15; 210(4):444-454.
-
Mattos WLLD, Khalil N, Spencer LG, Bonella F, Folz RJ, Rolf JD, Mogulkoc N, Lancaster LH, Jenkins RG, Lynch DA, Noble PW, Maher TM, Cottin V, Senger S, Horan GS, Greenberg S, Popmihajlov Z. Phase 2, Double-Blind, Placebo-controlled Trial of a c-Jun N-Terminal Kinase Inhibitor in Idiopathic Pulmonary Fibrosis. Am J Respir Crit Care Med. 2024 Aug 15; 210(4):435-443.
|
People  People who have written about this concept. _
Similar Concepts
People who have written about this concept.
_
Top Journals
Top journals in which articles about this concept have been published.
|